From: Primary adenoid cystic carcinoma of the breast: case report and review of the literature
Incidence: |
• 0.1% of all breast cancers. |
Age at presentation: |
• 30 to 90 (mostly in 5th and 6th decade of life). |
Most common presentation: |
• Painful breast mass. |
Mammography (role): |
• Limited as compared to other breast cancers (may miss the tumor). |
Lymph node involvement: |
• Uncommon. |
Metastases: |
• Rare (can occur without LN involvement). |
Most common site of metastases: |
• Lung. |
Management Options: |
Surgery |
• Simple Mastectomy (most widely performed). |
• Lumpectomy followed by radiation (alternative option). |
• Modified radical mastectomy (falling out of favor, considered too radical). |
Radiation: |
• Insufficiently evaluated (follows lumpectomy). |
Chemotherapy: |
• Not studied. |
Hormonal manipulation: |
• Of limited value as most cases are ER & PR negative. |